Coexistence of Hypertrophic Pyloric Stenosis and Long-gap Isolated Esophageal Atresia: A Case Report and Review of the Literature

Abstract

The coexistence of hypertrophic pyloric stenosis (HPS) and esophageal atresia (EA) is a rare condition. In the literature, also, there are only a few publications written about this rare coexistent condition. In this study, an incidental HPS case, which was discovered during gastric pull-up surgery for long-gap isolated EA, is investigated. A 50-day old girl who had isolated EA applied to our clinic for gastric pull-up surgery, which was planned to replace her currently existing gastrostomy which was performed in the newborn period. During the operation, it was seen that the stomach was larger than expected because of HPS. Pyloromyotomy was carried out before gastric pull-up. Following this, the stomach was pulled upwards from the mediastinum and anastomosed with the proximal esophagus. No complication developed during or after the surgery. In cases where patients with EA come with nutrition problems, and also stricture of the anastomosis line or gastroesophageal reflux are excluded, it should be kept in mind that the reason may be HPS.